Ketones bodies are alternate forms of energy currency in time of glucose debt. They are
- Acetoacetate
- \(\beta\)-hydroxybutyrate
- Acetone
Normally only \(\beta\)-hydroxybutyrate is measured. Normal value <0.6mM
Production
- Produced by liver
- Basaslly produced, production increases in starvation, hypoinsulinaemia, or when intracellular glucose is low
Metabolism - Ketogenesis
- Glucagon, catecholamines, and suppression of insulin \(\to\) liberation of FFAs from adipose tissue
- Fatty acids \(\to\) acetyl-CoA
- In low-glucose conditions, oxaloacetate (final step of Kreb's cycle) is consumed by gluconeogenesis \(\to\) Acetyl-CoA cannot enter Krebs cycle
- result in Acetyl-CoA accumulation in hepatic mitochondria
- condensation of 2 acetyl-CoA \(\to\) acetoacetate
- acetoacetate \(\xrightarrow{reduction}\) \(\beta\)-hydroxybutyrate
Metabolism - Ketolysis
- Converted back to acetyl-CoA in mitochondria \(\to\) enter Krebs cycle
Role
- Provide fuel for many extrahepatic cells
- Can cross BBB \(\to\) supply neurons